A rare incidence of pigmented paravenous retino-choroidal atrophy in rheumatoid arthritis

Pigmented paravenous retinochoroidal atrophy is a rare disease characterized by perivenous aggregations of pigment clumps associated with peripapillary and radial zones of retinochoroidal atrophy that are distributed along retinal veins. A 55-year-old female presented to our hospital with complaints of floaters in both eyes of 2 years duration. She is a known case of Dry eye and Rheumatoid arthritis on treatment. Fundoscopic examination found bony spicule pigmentation and retinochoroidal atrophy along the retinal veins, bilaterally without macular involvement or signs of inflammationSpectral domain optical coherence tomography imaging revealed lamellar macular hole and thinning of outer retina at the region of pigment deposition along the veins in both eyes. No intervention was done and was advised to follow up. Pigmented paravenous retinochoroidal atrophy is a rare disease characterized by perivenous aggregations of pigment clumps associated with peripapillary and radial zones of retinochoroidal atrophy that are distributed along retinal veins. It has been described in the literature in association with diseases like Behcet’s disease, Vogt Koyanagi Harada syndrome, measles, rubeola, tubercular spondylitis, syphilis, and sarcoidosis. PPRCA in a case of Rheumatoid arthritis, to our knowledge has not been reported.